Share this article

Congenital pulmonary lymphangiectasia

Elizabeth Doecke
15 December 2014

<p>Congenital pulmonary lymphangiectasia is a rare condition caused by failure of pulmonary lymphatic vessels to develop normally. It is a known cause of non-immune hydops fetalis and congenital chylothorax. While it has been recognised in the literature since the 1950s, no standardised treatment has yet emerged and a definitive cause is still unknown. This review seeks to draw together current information on diagnosis, treatment and prognosis, and to recommend that a systemic evaluation of such would provide direction for clinicians in dealing with patients aᰀected by this condition.</p>

Free for all healthcare professionals

Sign up to the Wounds Group journals

By clicking ‘Subscribe’, you are agreeing that the Wounds Group are able to email you periodic newsletters. You may unsubscribe from these at any time. Your info is safe with us and we will never sell or trade your details. For information please review our privacy policy.

Are you a healthcare professional? This website is for healthcare professionals only. To continue, please confirm that you are a healthcare professional below.

We use cookies responsibly to ensure that we give you the best experience on our website. If you continue without changing your browser settings, we’ll assume that you are happy to receive all cookies on this website. Read about how we use cookies.

I am not a healthcare professional.